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Trial details imported from ClinicalTrials.gov

For full trial details, please see the original record at https://clinicaltrials.gov/study/NCT04652726




Registration number
NCT04652726
Ethics application status
Date submitted
2/12/2020
Date registered
3/12/2020
Date last updated
10/06/2025

Titles & IDs
Public title
Study to Evaluate Efficacy and Safety of Inclisiran in Adolescents With Heterozygous Familial Hypercholesterolemia
Scientific title
Two Part (Double-blind Inclisiran Versus Placebo [Year 1] Followed by Open-label Inclisiran [Year 2]) Randomized Multicenter Study to Evaluate Safety, Tolerability, and Efficacy of Inclisiran in Adolescents (12 to Less Than 18 Years) With Heterozygous Familial Hypercholesterolemia and Elevated LDL-cholesterol (ORION-16)
Secondary ID [1] 0 0
2020-002757-18
Secondary ID [2] 0 0
CKJX839C12301
Universal Trial Number (UTN)
Trial acronym
ORION-16
Linked study record

Health condition
Health condition(s) or problem(s) studied:
Familial Hypercholesterolemia - Heterozygous 0 0
Condition category
Condition code
Metabolic and Endocrine 0 0 0 0
Other metabolic disorders
Human Genetics and Inherited Disorders 0 0 0 0
Other human genetics and inherited disorders

Intervention/exposure
Study type
Interventional
Description of intervention(s) / exposure
Treatment: Drugs - Inclisiran
Treatment: Drugs - Placebo

Experimental: Inclisiran - Year 1 - inclisiran sodium 300 mg subcutaneous injection (given at Days 1, 90, and 270) Day 360 only - placebo subcutaneous injection Year 2 - inclisiran sodium 300 mg subcutaneous injection (given at Days 450 and 630)

Placebo comparator: Placebo - Year 1 - placebo subcutaneous injection (given at Days 1, 90 and 270) Year 2 - inclisiran sodium 300 mg subcutaneous injection (given at Days 360, 450, and 630)


Treatment: Drugs: Inclisiran
Inclisiran sodium 300 mg (equivalent to 284 mg inclisiran) in 1.5 mL solution for subcutaneous injection

Treatment: Drugs: Placebo
Sterile normal saline (0.9% sodium chloride in water for subcutaneous injection)

Intervention code [1] 0 0
Treatment: Drugs
Comparator / control treatment
Control group

Outcomes
Primary outcome [1] 0 0
Percentage Change in LDL-C From Baseline to Day 330 (Part 1/Year 1)
Timepoint [1] 0 0
Baseline and Day 330
Secondary outcome [1] 0 0
Time-adjusted Percent Change in LDL-C From Baseline After Day 90 and up to Day 330 (Part 1/Year 1)
Timepoint [1] 0 0
Baseline, after Day 90 up to Day 330
Secondary outcome [2] 0 0
Absolute Change in LDL-C From Baseline to up Day 330 (Part 1/Year 1)
Timepoint [2] 0 0
Baseline and Day 330
Secondary outcome [3] 0 0
Percent Change in Apo B From Baseline up to Day 330 (Part 1/Year 1)
Timepoint [3] 0 0
Baseline and Day 330
Secondary outcome [4] 0 0
Percent Change in Lp(a) From Baseline up to Day 330 (Part 1/Year 1)
Timepoint [4] 0 0
Baseline and Day 330
Secondary outcome [5] 0 0
Percent Change in Non-HDL-C From Baseline up to Day 330 (Part 1/Year 1)
Timepoint [5] 0 0
Baseline and Day 330
Secondary outcome [6] 0 0
Percent Change in Total Cholesterol From Baseline up to Day 330 (Part 1/Year 1)
Timepoint [6] 0 0
Baseline and Day 330
Secondary outcome [7] 0 0
Percent Change in LDL-C From Baseline up to Day 720
Timepoint [7] 0 0
Baseline, up to Day 720
Secondary outcome [8] 0 0
Absolute Change in LDL-C From Baseline up to Day 720
Timepoint [8] 0 0
Baseline, up to Day 720
Secondary outcome [9] 0 0
Percent Change in Apo B From Baseline up to Day 720
Timepoint [9] 0 0
Baseline, up to Day 720
Secondary outcome [10] 0 0
Absolute Change in Apo B From Baseline up to Day 720
Timepoint [10] 0 0
Baseline, up to Day 720
Secondary outcome [11] 0 0
Percent Change in Lp(a) From Baseline up to Day 720
Timepoint [11] 0 0
Baseline, up to Day 720
Secondary outcome [12] 0 0
Absolute Change in Lp(a) From Baseline up to Day 720
Timepoint [12] 0 0
Baseline, up to Day 720
Secondary outcome [13] 0 0
Percent Change in Non-HDL-C From Baseline up to Day 720
Timepoint [13] 0 0
Baseline, up to Day 720
Secondary outcome [14] 0 0
Absolute Change in Non-HDL-C From Baseline up to Day 720
Timepoint [14] 0 0
Baseline, up to Day 720
Secondary outcome [15] 0 0
Percent Change in Total Cholesterol From Baseline up to Day 720
Timepoint [15] 0 0
Baseline, up to Day 720
Secondary outcome [16] 0 0
Absolute Change in Total Cholesterol From Baseline up to Day 720
Timepoint [16] 0 0
Baseline, up to Day 720
Secondary outcome [17] 0 0
Percent Change in Triglycerides From Baseline up to Day 720
Timepoint [17] 0 0
Baseline, up to Day 720
Secondary outcome [18] 0 0
Absolute Change in Triglycerides From Baseline up to Day 720
Timepoint [18] 0 0
Baseline, up to Day 720
Secondary outcome [19] 0 0
Percent Change in HDL-C From Baseline up to Day 720
Timepoint [19] 0 0
Baseline, up to Day 720
Secondary outcome [20] 0 0
Absolute Change in HDL-C From Baseline up to Day 720
Timepoint [20] 0 0
Baseline, up to Day 720
Secondary outcome [21] 0 0
Percent Change in VLDL-C From Baseline up to Day 720
Timepoint [21] 0 0
Baseline, up to Day 720
Secondary outcome [22] 0 0
Absolut Change in VLDL-C From Baseline up to Day 720
Timepoint [22] 0 0
Baseline, up to Day 720
Secondary outcome [23] 0 0
Percent Change in Apo A1 From Baseline up to Day 720
Timepoint [23] 0 0
Baseline, up to Day 720
Secondary outcome [24] 0 0
Absolute Change in Apo A1 From Baseline up to Day 720
Timepoint [24] 0 0
Baseline, up to Day 720
Secondary outcome [25] 0 0
Percent Change in PCSK9 From Baseline up to Day 720
Timepoint [25] 0 0
Baseline, up to Day 720
Secondary outcome [26] 0 0
Absolut Change in PCSK9 From Baseline up to Day 720
Timepoint [26] 0 0
Baseline, up to Day 720

Eligibility
Key inclusion criteria
* Heterozygous Familial Hypercholesterolemia (HeFH) diagnosed either by genetic testing or on phenotypic criteria
* Fasting LDL-C >130 mg/dL (3.4 mmol/L) at screening
* Fasting triglycerides <400 mg/dL (4.5 mmol/L) at screening
* On maximally tolerated dose of statin (investigator's discretion) with or without other lipid-lowering therapy; stable for = 30 days before screening
Minimum age
12 Years
Maximum age
17 Years
Sex
Both males and females
Can healthy volunteers participate?
No
Key exclusion criteria
* Homozygous familial hypercholesterolemia (HoFH)
* Active liver disease
* Secondary hypercholesterolemia, e.g. hypothyroidism or nephrotic syndrome
* Previous treatment with monoclonal antibodies directed towards PCSK9 (within 90 days of screening)
* Recent and/or planned use of other investigational medicinal products or devices

Study design
Purpose of the study
Treatment
Allocation to intervention
Randomised controlled trial
Procedure for enrolling a subject and allocating the treatment (allocation concealment procedures)
Methods used to generate the sequence in which subjects will be randomised (sequence generation)
Masking / blinding
Blinded (masking used)
Who is / are masked / blinded?
The people receiving the treatment/s


The people analysing the results/data
Intervention assignment
Parallel
Other design features
Phase
Phase 3
Type of endpoint/s
Statistical methods / analysis

Recruitment
Recruitment status
Completed
Data analysis
Reason for early stopping/withdrawal
Other reasons
Date of first participant enrolment
Anticipated
Actual
Date of last participant enrolment
Anticipated
Actual
Date of last data collection
Anticipated
Actual
Sample size
Target
Accrual to date
Final
Recruitment in Australia
Recruitment state(s)
Recruitment outside Australia
Country [1] 0 0
United States of America
State/province [1] 0 0
Arizona
Country [2] 0 0
United States of America
State/province [2] 0 0
New York
Country [3] 0 0
United States of America
State/province [3] 0 0
North Carolina
Country [4] 0 0
United States of America
State/province [4] 0 0
Ohio
Country [5] 0 0
United States of America
State/province [5] 0 0
Pennsylvania
Country [6] 0 0
United States of America
State/province [6] 0 0
Utah
Country [7] 0 0
Argentina
State/province [7] 0 0
Formosa
Country [8] 0 0
Brazil
State/province [8] 0 0
Ceara
Country [9] 0 0
Brazil
State/province [9] 0 0
RS
Country [10] 0 0
Brazil
State/province [10] 0 0
SP
Country [11] 0 0
Canada
State/province [11] 0 0
Quebec
Country [12] 0 0
Czechia
State/province [12] 0 0
Praha 5
Country [13] 0 0
Czechia
State/province [13] 0 0
Praha
Country [14] 0 0
France
State/province [14] 0 0
Besancon Cedex
Country [15] 0 0
France
State/province [15] 0 0
Bron Cedex
Country [16] 0 0
France
State/province [16] 0 0
Toulouse Cedex
Country [17] 0 0
Germany
State/province [17] 0 0
Baden-Wuerttemberg
Country [18] 0 0
Germany
State/province [18] 0 0
Frankfurt
Country [19] 0 0
Germany
State/province [19] 0 0
Freiburg
Country [20] 0 0
Greece
State/province [20] 0 0
GR
Country [21] 0 0
Greece
State/province [21] 0 0
Athens
Country [22] 0 0
Hungary
State/province [22] 0 0
Pecs
Country [23] 0 0
Israel
State/province [23] 0 0
Jerusalem
Country [24] 0 0
Israel
State/province [24] 0 0
Ramat Gan
Country [25] 0 0
Italy
State/province [25] 0 0
MI
Country [26] 0 0
Italy
State/province [26] 0 0
MO
Country [27] 0 0
Italy
State/province [27] 0 0
RM
Country [28] 0 0
Jordan
State/province [28] 0 0
Irbid
Country [29] 0 0
Lebanon
State/province [29] 0 0
Ashrafieh
Country [30] 0 0
Malaysia
State/province [30] 0 0
Selangor Darul Ehsan
Country [31] 0 0
Netherlands
State/province [31] 0 0
Zuid Holland
Country [32] 0 0
Netherlands
State/province [32] 0 0
Amsterdam
Country [33] 0 0
Norway
State/province [33] 0 0
Oslo
Country [34] 0 0
Poland
State/province [34] 0 0
Gdansk
Country [35] 0 0
Poland
State/province [35] 0 0
Lodz
Country [36] 0 0
Russian Federation
State/province [36] 0 0
Kemerovo
Country [37] 0 0
Russian Federation
State/province [37] 0 0
Moscow
Country [38] 0 0
Russian Federation
State/province [38] 0 0
Novosibirsk
Country [39] 0 0
Slovakia
State/province [39] 0 0
Poprad
Country [40] 0 0
Slovenia
State/province [40] 0 0
Ljubljana
Country [41] 0 0
South Africa
State/province [41] 0 0
Free State
Country [42] 0 0
South Africa
State/province [42] 0 0
Western Cape
Country [43] 0 0
South Africa
State/province [43] 0 0
Cape Town
Country [44] 0 0
Spain
State/province [44] 0 0
Andalucia
Country [45] 0 0
Spain
State/province [45] 0 0
Asturias
Country [46] 0 0
Spain
State/province [46] 0 0
Navarra
Country [47] 0 0
Spain
State/province [47] 0 0
A Coruna
Country [48] 0 0
Switzerland
State/province [48] 0 0
Geneve 14
Country [49] 0 0
Taiwan
State/province [49] 0 0
New Taipei
Country [50] 0 0
Taiwan
State/province [50] 0 0
Taipei
Country [51] 0 0
Turkey
State/province [51] 0 0
TUR
Country [52] 0 0
Turkey
State/province [52] 0 0
Adana
Country [53] 0 0
Turkey
State/province [53] 0 0
Ankara
Country [54] 0 0
Turkey
State/province [54] 0 0
Izmir
Country [55] 0 0
United Kingdom
State/province [55] 0 0
Middlesex

Funding & Sponsors
Primary sponsor type
Commercial sector/industry
Name
Novartis Pharmaceuticals
Address
Country

Ethics approval
Ethics application status

Summary
Brief summary
Trial website
Trial related presentations / publications
Public notes

Contacts
Principal investigator
Name 0 0
Novartis Pharmaceuticals
Address 0 0
Novartis Pharmaceuticals
Country 0 0
Phone 0 0
Fax 0 0
Email 0 0
Contact person for public queries
Name 0 0
Address 0 0
Country 0 0
Phone 0 0
Fax 0 0
Email 0 0
Contact person for scientific queries

Data sharing statement
Will individual participant data (IPD) for this trial be available (including data dictionaries)?
Yes
What data in particular will be shared?
Novartis is committed to sharing with qualified external researchers, access to patient-level data and supporting clinical documents from eligible studies. These requests are reviewed and approved by an independent review panel on the basis of scientific merit. All data provided is anonymized to respect the privacy of patients who have participated in the trial in line with applicable laws and regulations.

This trial data availability is according to the criteria and process described on www.clinicalstudydatarequest.com.
When will data be available (start and end dates)?
Available to whom?
Available for what types of analyses?
How or where can data be obtained?


What supporting documents are/will be available?

Results publications and other study-related documents

No documents have been uploaded by study researchers.